Gene: [09^/CPO] coproporphyrinogen oxidase; harderoporphyrinuria (coproporphyria);

FUN

[1] Systematic name: coproporphyrinogen:oxygen oxidoreductase.
[2] Catalyzes reaction: coproporphyrinogen-III + O(2) = protoporphyrinogen-IX + 2 CO(2)."

HET

There are several loci responsible for various types of porphyria in the human genome. On the classification of hereditary porphyrias, see GEM:01p34/UROD."

REF

HIS,IDN,PAT "Berger, Goldberg: Brit Med J, 2, 85-88, 1955
LOC,CYG "Grandchamp B &: Hum Genet, 64, 180-183, 1983
MEB,FUN,PAT "McColl KE, Goldberg: Biochem Soc Trans, 11, 631-632, 1983

SWI

 SWISSPROT: P36551

KEY

git, mito, mtbd

CLA

coding, basic

LOC

09

MIM

 MIM: 121300

EZN

 ENZYME: 1.3.3.3